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paraganglioma

^ http://purl.obolibrary.org/obo/MONDO_0000448

A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. [ NCIT:C3308 ]

Term info

database cross reference
  • EFO:1000453 (MONDO:equivalentTo)
  • SCTID:127027008 (MONDO:equivalentTo)
  • NCIT:C3308 (MONDO:equivalentTo)
  • DOID:0050773 (MONDO:equivalentTo)
  • ICDO:8680/1 (NCIT:C3308)
  • OMIMPS:168000 (MONDO:equivalentTo)
  • MESH:D010235 (MONDO:equivalentTo)
  • ICD9:239.7 (MONDO:relatedTo)
  • UMLS:C0030421 (NCIT:C3308)
  • ONCOTREE:PGNG (MONDO:equivalentTo)
definition

A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases.

exactMatch

http://identifiers.org/snomedct/127027008, https://omim.org/phenotypicSeries/PS168000, http://purl.obolibrary.org/obo/DOID_0050773, http://identifiers.org/mesh/D010235, http://purl.obolibrary.org/obo/NCIT_C3308, http://linkedlifedata.com/resource/umls/id/C0030421

has exact synonym

neoplasm of the paraganglion, neoplasm of paraganglion, paraganglion neoplasm, paragangliomas, tumor of the paraganglion, tumor of paraganglion, Paraganglionic neoplasm, paraganglion tumor, Paraganglionic tumor, paraganglioma

has narrow synonym

chemodectoma

id

MONDO:0000448