Term info
- ICD9:171.9 (MONDO:relatedTo)
- NCIT:C4247 (MONDO:equivalentTo)
- DOID:1907 (MONDO:equivalentTo)
- EFO:1001972 (MONDO:equivalentTo)
- GARD:0006963 (MONDO:equivalentTo)
- HGNC:16982 (GARD:0006963)
- MedDRA:10025552 (Orphanet:2023/e)
- NCIT:C114541 (MONDO:equivalentTo)
- ICDO:8830/3 (NCIT:C4247)
- Orphanet:2023 (MONDO:equivalentTo)
- ONCOTREE:MFH (MONDO:equivalentTo)
- SCTID:443439001 (MONDO:equivalentTo)
- MESH:D051677 (Orphanet:2023/e)
gard_rare, ordo_disease
http://identifiers.org/meddra/10025552
An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma.
http://purl.obolibrary.org/obo/DOID_1907, http://purl.obolibrary.org/obo/NCIT_C4247, http://identifiers.org/mesh/D051677, http://identifiers.org/snomedct/443439001, http://purl.obolibrary.org/obo/NCIT_C114541, http://purl.obolibrary.org/obo/Orphanet_2023
MONDO:0016069
malignant fibrous histiocytoma, Storiform-pleomorphic MFH, Unclassified Pleomorphic sarcoma (formerly "malignant fibrous histiocytoma"), malignant fibrous histiocytoma of the soft tissue and bone, Storiform-pleomorphic fibrous histiocytoma, histiocytoma, fibrous, malignant, adult malignant fibrous histiocytoma, MFH, Storiform-pleomorphic malignant fibrous histiocytoma, fibrous histiocytoma, malignant (morphologic abnormality), undifferentiated pleomorphic sarcoma, unclassified pleomorphic sarcoma, fibroxanthosarcoma, malignant fibrous histiocytoma of soft tissue and bone, fibrous histiocytoma, malignant, adult undifferentiated pleomorphic sarcoma, Unclassified Pleomorphic sarcoma (formerly "MFH"), malignant fibrous cytoma, UPS, malignant fibroxanthoma, undifferentiated pleomorphic soft tissue sarcoma, fibroxanthosarcoma (morphologic abnormality), adult unclassified pleomorphic sarcoma
malignant fibrohistiocytic tumors, undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma
MONDO:0002142
https://rarediseases.info.nih.gov/diseases/6963/undifferentiated-pleomorphic-sarcoma