JSON

adamantinoma

^ http://purl.obolibrary.org/obo/MONDO_0002422


A low grade malignant neoplasm arising from the long bones. The tibia is the most frequently affected bone site. Patients present with swelling which may or may not be associated with pain. Morphologically, it is characterized by a biphasic pattern consisting of an epithelial and an osteofibrous component. The vast majority of cases recur if they are not treated with radical surgery. In a minority of cases the tumor may metastasize to other anatomic sites including lymph nodes, lungs, liver, brain, and skeleton. [ NCIT:C7644 ]

Term info

database cross reference
  • MESH:D050398 (Orphanet:55881/e)
  • Orphanet:55881 (OMIM:102660)
  • DOID:2776 (MONDO:equivalentTo)
  • SCTID:307609003 (MONDO:equivalentTo)
  • MESH:C562741 (MONDO:equivalentTo)
  • NCIT:C7644 (MONDO:equivalentTo)
  • UMLS:C0334556 (OMIM:102660)
  • OMIM:102660 (Orphanet:55881/e)
  • DOID:2775 (MONDO:equivalentTo)
  • UMLS:C1367554 (Orphanet:55881/e)
  • ICD9:170.9 (MONDO:relatedTo)
  • ONCOTREE:ADMA (MONDO:equivalentTo)
  • ICDO:9261/3 (NCIT:C7644)
  • ICD10CM:C40.2 (Orphanet:55881/ntbt)
Subsets

ordo_disease

definition

A low grade malignant neoplasm arising from the long bones. The tibia is the most frequently affected bone site. Patients present with swelling which may or may not be associated with pain. Morphologically, it is characterized by a biphasic pattern consisting of an epithelial and an osteofibrous component. The vast majority of cases recur if they are not treated with radical surgery. In a minority of cases the tumor may metastasize to other anatomic sites including lymph nodes, lungs, liver, brain, and skeleton.

exactMatch

http://purl.obolibrary.org/obo/DOID_2775, http://purl.obolibrary.org/obo/DOID_2776, http://identifiers.org/mesh/D050398, http://purl.obolibrary.org/obo/NCIT_C7644, http://identifiers.org/snomedct/307609003, http://identifiers.org/mesh/C562741, http://linkedlifedata.com/resource/umls/id/C0334556, https://omim.org/entry/102660, http://purl.obolibrary.org/obo/Orphanet_55881

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0015959

has exact synonym

Extragnathic adamantinoma, long bone adamantinoma, adamantinoma of long bones, adamantinoma of long bones (morphologic abnormality), adamantinoma, malignant, adamantinoma

has related synonym

adamantinoma of long bone

id

MONDO:0002422

Term relations

Subclass of: