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pancreatic acinar cell carcinoma

^ http://purl.obolibrary.org/obo/MONDO_0006346


An adenocarcinoma arising from the pancreas. It is characterized by the presence of relatively uniform malignant cells which form acinar patterns. It usually occurs during adulthood. Signs and symptoms include abdominal pain, weight loss, nausea, and diarrhea. It may metastasize to regional lymph nodes and the liver. A minority of patients develop lipase hypersecretion syndrome. This syndrome may be seen in patients with liver metastases and it is characterized by excessive secretion of lipase in the serum, polyarthralgia, and subcutaneous fat necrosis. [ NCIT:C7977 ]

Term info

database cross reference
  • UMLS:C0279661 (Orphanet:424046)
  • DOID:5742 (MONDO:equivalentTo)
  • EFO:1000439 (MONDO:equivalentTo)
  • Orphanet:424046 (MONDO:equivalentTo)
  • NCIT:C7977 (MONDO:equivalentTo)
  • ONCOTREE:PAAC (MONDO:equivalentTo)
Subsets

ordo_disease

abbreviation
PAAC [ ONCOTREE:PAAC ]

definition

An adenocarcinoma arising from the pancreas. It is characterized by the presence of relatively uniform malignant cells which form acinar patterns. It usually occurs during adulthood. Signs and symptoms include abdominal pain, weight loss, nausea, and diarrhea. It may metastasize to regional lymph nodes and the liver. A minority of patients develop lipase hypersecretion syndrome. This syndrome may be seen in patients with liver metastases and it is characterized by excessive secretion of lipase in the serum, polyarthralgia, and subcutaneous fat necrosis.

exactMatch

http://purl.obolibrary.org/obo/NCIT_C7977, http://purl.obolibrary.org/obo/DOID_5742, http://purl.obolibrary.org/obo/Orphanet_424046, http://linkedlifedata.com/resource/umls/id/C0279661

has exact synonym

Pancreatic acinar cell cancer, acinar cell adenocarcinoma of the pancreas, pancreas acinar cell adenocarcinoma, carcinoma of pancreatic acinar cell, acinar cell adenocarcinoma of pancreas, pancreatic acinar cell adenocarcinoma, acinar cell carcinoma of pancreas, pancreatic acinar cell carcinoma, acinar cell carcinoma of the pancreas

id

MONDO:0006346