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neoplasm with perivascular epithelioid cell differentiation

^ http://purl.obolibrary.org/obo/MONDO_0006359

A soft tissue neoplasm composed of perivascular epithelioid cells. Representative examples include angiomyolipoma, clear cell-sugar-tumor of the lung, and lymphangioleiomyomatosis. [ NCIT:C38150 ]

Term info

database cross reference
  • NCIT:C38150 (MONDO:equivalentTo)
  • ONCOTREE:PECOMA (MONDO:equivalentTo)
  • Orphanet:595133 (MONDO:equivalentTo)
  • MESH:D054973 (MONDO:equivalentTo)
  • DOID:2643 (MONDO:equivalentTo)
  • EFO:1000464 (MONDO:equivalentTo)
  • UMLS:C1300127 (NCIT:C38150)
Subsets

ordo_disease

comment

MeSH defintion: A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. These cells do not have a normal anatomic homolog. (From Fletcher CDM, et. al., World Health Organization Classification of Tumors: Pathology and Genetics of Tumors of Soft Tissue and Bone, 2002).

definition

A soft tissue neoplasm composed of perivascular epithelioid cells. Representative examples include angiomyolipoma, clear cell-sugar-tumor of the lung, and lymphangioleiomyomatosis.

exactMatch

http://purl.obolibrary.org/obo/DOID_2643, http://purl.obolibrary.org/obo/NCIT_C38150, http://identifiers.org/mesh/D054973, http://linkedlifedata.com/resource/umls/id/C1300127, http://purl.obolibrary.org/obo/Orphanet_595133

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0002604

has exact synonym

tumor with perivascular epithelioid cell differentiation, perivascular epithelioid cell tumor, PEComa, neoplasm with perivascular epithelioid cell differentiation

id

MONDO:0006359

Term relations

Subclass of: