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peritoneal multicystic mesothelioma

^ http://purl.obolibrary.org/obo/MONDO_0006363


A cystic mesothelioma that arises from the peritoneum and usually affects young to middle aged females. Grossly, it presents as a large multiloculated tumor mass, usually in the pelvic peritoneum. Histologically it is characterized by the presence of multiple cysts that are lined by one or more layers of mesothelial cells that do not show atypia. Patients usually present with abdominal or pelvic mass and pain. The clinical course is indolent. The tumor may recur, but transformation to diffuse malignant mesothelioma is rare. [ NCIT:C6536 ]

Term info

database cross reference
  • SCTID:716650003 (MONDO:equivalentTo)
  • EFO:1000468 (MONDO:equivalentTo)
  • NCIT:C6536 (MONDO:equivalentTo)
  • UMLS:C1334818 (NCIT:C6536)
  • Orphanet:168816 (MONDO:equivalentTo)
  • GARD:0010777 (MONDO:equivalentTo)
Subsets

ordo_disease

abbreviation
BMPM [ GARD:0010777 ]

definition

A cystic mesothelioma that arises from the peritoneum and usually affects young to middle aged females. Grossly, it presents as a large multiloculated tumor mass, usually in the pelvic peritoneum. Histologically it is characterized by the presence of multiple cysts that are lined by one or more layers of mesothelial cells that do not show atypia. Patients usually present with abdominal or pelvic mass and pain. The clinical course is indolent. The tumor may recur, but transformation to diffuse malignant mesothelioma is rare.

exactMatch

http://identifiers.org/snomedct/716650003, http://purl.obolibrary.org/obo/NCIT_C6536, http://linkedlifedata.com/resource/umls/id/C1334818, http://purl.obolibrary.org/obo/Orphanet_168816

has exact synonym

multicystic mesothelioma of peritoneum, peritoneal cystic mesothelioma, peritoneal multicystic mesothelioma, multicystic mesothelioma, multilocular peritoneal inclusion cyst, multicystic mesothelioma of the peritoneum

has narrow synonym

benign multicystic peritoneal mesothelioma

has related synonym

multilocular peritoneal inclusion cysts, BMPM, multilocular peritoneal cysts, benign cystic peritoneal mesothelioma

id

MONDO:0006363