small intestinal enteropathy-associated T-cell lymphoma
An enteropathy-associated T-cell lymphoma arising from the small intestine, most commonly the jejunum or ileum. Patients usually present with abdominal pain, often associated with intestinal perforation. There is often a history of celiac disease. The lymphoma cells are usually medium-sized to large and form an ulcerating mucosal lesion with invasion of the small intestinal wall. Villous atrophy is present in the adjacent small intestinal mucosa. In a minority of cases the lymphoma cells are medium-sized and form a monomorphic infiltrate. [ NCIT:P378 ]
Term info
- NCIT:C39610 (MONDO:equivalentTo)
- UMLS:C1519371 (NCIT:C39610)
- EFO:1000535 (MONDO:equivalentTo)
An enteropathy-associated T-cell lymphoma arising from the small intestine, most commonly the jejunum or ileum. Patients usually present with abdominal pain, often associated with intestinal perforation. There is often a history of celiac disease. The lymphoma cells are usually medium-sized to large and form an ulcerating mucosal lesion with invasion of the small intestinal wall. Villous atrophy is present in the adjacent small intestinal mucosa. In a minority of cases the lymphoma cells are medium-sized and form a monomorphic infiltrate.
http://linkedlifedata.com/resource/umls/id/C1519371, http://purl.obolibrary.org/obo/NCIT_C39610
small intestinal EATL, small intestinal enteropathy-type T-cell lymphoma, enteropathy-associated T-cell lymphoma of small intestine, small intestine enteropathy-associated T-cell lymphoma
MONDO:0006418