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malignant atrophic papulosis

^ http://purl.obolibrary.org/obo/MONDO_0011208

Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal. [ Orphanet:679 ]

Term info

database cross reference
  • MESH:D054853 (Orphanet:679/e)
  • SCTID:400171002 (MONDO:equivalentTo)
  • Orphanet:679 (OMIM:602248)
  • ICD9:447.8 (MONDO:relatedTo)
  • OMIM:602248 (Orphanet:679/e)
  • MedDRA:10064281 (Orphanet:679/e)
  • UMLS:C0221011 (Orphanet:679/e)
  • GARD:0006249 (MONDO:equivalentTo)
  • NCIT:C84835 (MONDO:equivalentTo)
Subsets

ordo_disease

closeMatch

http://identifiers.org/meddra/10064281

definition

Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal.

exactMatch

https://omim.org/entry/602248, http://purl.obolibrary.org/obo/NCIT_C84835, http://identifiers.org/mesh/D054853, http://linkedlifedata.com/resource/umls/id/C0221011, http://identifiers.org/snomedct/400171002, http://purl.obolibrary.org/obo/Orphanet_679

has exact synonym

papulosis atrophican maligna, Köhlmeier-Degos disease, Kohlmeier-Degos-Delort-Tricort syndrome, Degos disease, Köhlmeier-Degos-Delort-Tricort syndrome, Kohlmeier-Degos disease, malignant atrophic papulosis

has related synonym

atrophic papulosis, malignant, Degos syndrome, papulosis, malignant atrophic, Degos's malignant atrophic papulosis

id

MONDO:0011208

Term relations