JSON

progressive non-fluent aphasia

^ http://purl.obolibrary.org/obo/MONDO_0015059

Progressive non-fluent aphasia (PNFA) is a form of frontotemporal dementia (FTD), characterized by agrammatism, laborious speech, alexia, and agraphia, frequently accompanied by apraxia of speech (AOS). Language comprehension is relatively preserved. [ Orphanet:100070 ]

Term info

database cross reference
  • Orphanet:100070 (MONDO:equivalentTo)
  • MESH:D057178 (Orphanet:100070/e)
  • GARD:0010793 (MONDO:equivalentTo)
  • SCTID:716281000 (MONDO:equivalentTo)
  • MedDRA:10029542 (Orphanet:100070/e)
  • NCIT:C85025 (MONDO:equivalentTo)
Subsets

gard_rare, ordo_disease

closeMatch

http://identifiers.org/meddra/10029542

definition

Progressive non-fluent aphasia (PNFA) is a form of frontotemporal dementia (FTD), characterized by agrammatism, laborious speech, alexia, and agraphia, frequently accompanied by apraxia of speech (AOS). Language comprehension is relatively preserved.

exactMatch

http://purl.obolibrary.org/obo/Orphanet_100070, http://identifiers.org/mesh/D057178, http://identifiers.org/snomedct/716281000, http://purl.obolibrary.org/obo/NCIT_C85025

has exact synonym

non-fluent variant PPA, Agramatic variant of PPA, Agramatic variant of primary progressive aphasia, Primary Progressive Nonfluent aphasia

has related synonym

non-fluent primary progressive aphasia

id

MONDO:0015059

seeAlso

https://rarediseases.info.nih.gov/diseases/10793/progressive-non-fluent-aphasia