ependymoma
A WHO grade II, slow growing tumor of children and young adults, usually located intraventricularly. It is the most common ependymal neoplasm. It often causes clinical symptoms by blocking cerebrospinal fluid pathways. Key histological features include perivascular pseudorosettes and ependymal rosettes. (WHO) [ NCIT:C3017 ]
Term info
- ONCOTREE:EPM (MONDO:equivalentTo)
- MedDRA:10014967 (Orphanet:251636/e)
- Orphanet:251636 (UMLS:CN201941)
- NCIT:C3017 (ONCOTREE:EPM)
- DOID:4844 (MONDO:equivalentTo)
- ICDO:9391/3 (NCIT:C3017)
- GARD:0006353 (MONDO:equivalentTo)
- MESH:D004806 (MONDO:equivalentTo)
- UMLS:CN201941 (MONDO:equivalentTo)
- UMLS:C0014474 (Orphanet:251636/e)
ordo_histopathological_subtype
http://identifiers.org/meddra/10014967
A WHO grade II, slow growing tumor of children and young adults, usually located intraventricularly. It is the most common ependymal neoplasm. It often causes clinical symptoms by blocking cerebrospinal fluid pathways. Key histological features include perivascular pseudorosettes and ependymal rosettes. (WHO)
http://purl.obolibrary.org/obo/DOID_4844, http://linkedlifedata.com/resource/umls/id/CN201941, http://purl.obolibrary.org/obo/NCIT_C3017, http://identifiers.org/mesh/D004806, http://linkedlifedata.com/resource/umls/id/C0014474, http://purl.obolibrary.org/obo/Orphanet_251636
http://purl.obolibrary.org/obo/MONDO_0000638, http://purl.obolibrary.org/obo/MONDO_0016697
ependymoma, epithelial ependymoma, benign ependymoma
ependymoma, benign, WHO grade II ependymal tumor, WHO grade II ependymal neoplasm
clear cell ependymoma (histologic variant), papillary ependymoma (histologic variant), ependymoma, familial, tanycytic ependymoma (histologic variant)
MONDO:0016698