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marginal zone lymphoma

^ http://purl.obolibrary.org/obo/MONDO_0017604

A usually indolent mature B-cell lymphoma, arising from the marginal zone of lymphoid tissues. It is characterized by the presence of small to medium sized atypical lymphocytes. It comprises three entities, according to the anatomic sites involved: extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue, which affects extranodal sites (most often stomach, lung, skin, and ocular adnexa); nodal marginal zone B-cell lymphoma, which affects lymph nodes without evidence of extranodal disease; and splenic marginal zone B-cell lymphoma, which affects the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood. [ NCIT:C4341 ]

Term info

database cross reference
  • ONCOTREE:MZL (MONDO:equivalentTo)
  • DOID:0050748 (MONDO:equivalentTo)
  • Orphanet:300912 (MONDO:equivalentTo)
  • SCTID:447100004 (MONDO:equivalentTo)
  • NCIT:C4341 (MONDO:equivalentTo)
  • GARD:0013237 (MONDO:equivalentTo)
  • UMLS:C1367654 (NCIT:C4341)
  • ICDO:9699/3 (NCIT:C4341)
  • EFO:1000630 (MONDO:equivalentTo)
Subsets

disease_grouping, ordo_group_of_disorders

abbreviation
MZL [ NCIT:C4341 ]

abbreviation
MZBCL [ NCIT:C4341 ]

definition

A usually indolent mature B-cell lymphoma, arising from the marginal zone of lymphoid tissues. It is characterized by the presence of small to medium sized atypical lymphocytes. It comprises three entities, according to the anatomic sites involved: extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue, which affects extranodal sites (most often stomach, lung, skin, and ocular adnexa); nodal marginal zone B-cell lymphoma, which affects lymph nodes without evidence of extranodal disease; and splenic marginal zone B-cell lymphoma, which affects the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood.

exactMatch

http://purl.obolibrary.org/obo/NCIT_C4341, http://purl.obolibrary.org/obo/DOID_0050748, http://purl.obolibrary.org/obo/Orphanet_300912, http://identifiers.org/snomedct/447100004, http://linkedlifedata.com/resource/umls/id/C1367654

has exact synonym

marginal zone B cell lymphoma, marginal zone B-cell lymphoma, MZBCL, MZL, marginal zone lymphoma, lymphoma of marginal zone B cell

id

MONDO:0017604