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idiopathic macular telangiectasia type 1

^ http://purl.obolibrary.org/obo/MONDO_0018146

A rare, acquired, eye disease characterized by unilateral (rarely bilateral) abnormally dilated and tortuous capillaries around the fovea, associated with multiple arteriolar and venular aneurysms, lipid depositions, and intra-retinal cystoid degeneration. It leads to vision loss due to macular edema with hard exudates. [ Orphanet:353344 ]

Term info

database cross reference
  • UMLS:CN204544 (MONDO:equivalentTo)
  • ICD10CM:H35.5 (Orphanet:353344/ntbt)
  • Orphanet:353344 (MONDO:equivalentTo)
Subsets

ordo_disease

definition

A rare, acquired, eye disease characterized by unilateral (rarely bilateral) abnormally dilated and tortuous capillaries around the fovea, associated with multiple arteriolar and venular aneurysms, lipid depositions, and intra-retinal cystoid degeneration. It leads to vision loss due to macular edema with hard exudates.

exactMatch

http://purl.obolibrary.org/obo/Orphanet_353344, http://linkedlifedata.com/resource/umls/id/CN204544

has exact synonym

aneurysmal telangiectasia, visible and exudative idiopathic juxtafoveolar retinal telangiectasis

id

MONDO:0018146

Term relations