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hydroa vacciniforme-like lymphoma

^ http://purl.obolibrary.org/obo/MONDO_0018224

A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin. [ NCIT:P378 ]

Term info

database cross reference
  • ICDO:9725/3 (NCIT:C45327)
  • Orphanet:364039 (MONDO:equivalentTo)
  • NCIT:C45327 (MONDO:equivalentTo)
  • UMLS:C1708397 (NCIT:C45327)
  • SCTID:763719001 (MONDO:equivalentTo)
Subsets

ordo_disease

abbreviation
HVLL [ Orphanet:364039 ]

definition

A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin.

exactMatch

http://purl.obolibrary.org/obo/NCIT_C45327, http://purl.obolibrary.org/obo/Orphanet_364039, http://identifiers.org/snomedct/763719001, http://linkedlifedata.com/resource/umls/id/C1708397

has exact synonym

hydroa vacciniforme-like cutaneous T-cell lymphoma, hV-like lymphoma, angiocentric cutaneous T-cell lymphoma of childhood, hydroa-like cutaneous T-cell lymphoma, hydroa vacciniforme-like lymphoma, hydroa vacciniforme-like lymphoproliferative disorder, HVLL

id

MONDO:0018224