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mucinous adenocarcinoma of the appendix

^ http://purl.obolibrary.org/obo/MONDO_0018330

Mucinous adenocarcinoma of the appendix is a very rare, slow growing, well-differentiated epithelial neoplasm of the appendix characterized by abundant mucin production. Clinically, it presents as acute appendicitis (with abdominal pain, fever, leukocytosis) or as pseudomyxoma peritonei (wide-spread presence of mucin within the peritoneal cavity), however some patients may be completely asymptomatic at the time of diagnosis. In many cases, a second gastrointestinal malignancy is present. [ Orphanet:391723 ]

Term info

database cross reference
  • Orphanet:391723 (MONDO:equivalentTo)
  • ONCOTREE:MAAP (MONDO:equivalentTo)
  • NCIT:C43558 (MONDO:exact-label-match)
  • UMLS:C1706832 (Orphanet:391723)
Subsets

ordo_disease

definition

Mucinous adenocarcinoma of the appendix is a very rare, slow growing, well-differentiated epithelial neoplasm of the appendix characterized by abundant mucin production. Clinically, it presents as acute appendicitis (with abdominal pain, fever, leukocytosis) or as pseudomyxoma peritonei (wide-spread presence of mucin within the peritoneal cavity), however some patients may be completely asymptomatic at the time of diagnosis. In many cases, a second gastrointestinal malignancy is present.

exactMatch

http://purl.obolibrary.org/obo/NCIT_C43558, http://linkedlifedata.com/resource/umls/id/C1706832, http://purl.obolibrary.org/obo/Orphanet_391723

has exact synonym

appendix mucinous adenocarcinoma, appendiceal mucinous adenocarcinoma, vermiform appendix mucinous adenocarcinoma

id

MONDO:0018330