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clear cell papillary renal cell carcinoma

^ http://purl.obolibrary.org/obo/MONDO_0018448

Clear cell papillary renal cell carcinoma is a rare, indolent subtype of clear cell renal carcinoma, arising from epithelial cells in the renal cortex. It most frequently manifests with a well-circumscribed, well-encapsulated, unicentric, unilateral, small tumor that typically does not metastasize. Clinically it can present with flank or abdominal pain or hematuria, although most patients are usually asymptomatic at the time of diagnosis. Bilateral and/or multifocal presentation should raise the suspicion of von Hippel-Lindau syndrome. [ Orphanet:404511 ]

Term info

database cross reference
  • ONCOTREE:CCPRC (MONDO:equivalentTo)
  • UMLS:C4518333 (MONDO:equivalentTo)
  • Orphanet:404511 (MONDO:equivalentTo)
  • SCTID:734015000 (MONDO:equivalentTo)
Subsets

ordo_histopathological_subtype

definition

Clear cell papillary renal cell carcinoma is a rare, indolent subtype of clear cell renal carcinoma, arising from epithelial cells in the renal cortex. It most frequently manifests with a well-circumscribed, well-encapsulated, unicentric, unilateral, small tumor that typically does not metastasize. Clinically it can present with flank or abdominal pain or hematuria, although most patients are usually asymptomatic at the time of diagnosis. Bilateral and/or multifocal presentation should raise the suspicion of von Hippel-Lindau syndrome.

exactMatch

http://identifiers.org/snomedct/734015000, http://purl.obolibrary.org/obo/Orphanet_404511, http://linkedlifedata.com/resource/umls/id/C4518333

id

MONDO:0018448

Term relations