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acquired cystic disease-associated renal cell carcinoma

^ http://purl.obolibrary.org/obo/MONDO_0018449


Acquired cystic disease-associated renal cell carcinoma is a rare subtype of renal cell carcinoma, ocurring in the context of end-stage kidney disease and acquired cystic kidney disease, characterized by a usually well circumscribed, solid, multifocal, bilateral tumor with inter- or intracellular microlumen formation (leading to cribiform architecture). Tumors are often diagnosed incidentally in early stages, although complications caused by renal cysts (dull flank or abdominal pain, fever) or renal parenchymal bleeding may mask the underlying neoplastic process. Most have an indolent behavior. [ Orphanet:404514 ]

Term info

database cross reference
  • UMLS:CN226194 (MONDO:equivalentTo)
  • Orphanet:404514 (MONDO:equivalentTo)
  • NCIT:C157718 (MONDO:equivalentTo)
Subsets

ordo_disease

definition

Acquired cystic disease-associated renal cell carcinoma is a rare subtype of renal cell carcinoma, ocurring in the context of end-stage kidney disease and acquired cystic kidney disease, characterized by a usually well circumscribed, solid, multifocal, bilateral tumor with inter- or intracellular microlumen formation (leading to cribiform architecture). Tumors are often diagnosed incidentally in early stages, although complications caused by renal cysts (dull flank or abdominal pain, fever) or renal parenchymal bleeding may mask the underlying neoplastic process. Most have an indolent behavior.

exactMatch

http://linkedlifedata.com/resource/umls/id/CN226194, http://purl.obolibrary.org/obo/Orphanet_404514, http://purl.obolibrary.org/obo/NCIT_C157718

id

MONDO:0018449

Term relations

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