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pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis

^ http://purl.obolibrary.org/obo/MONDO_0018554

A rare subgroup of pulmonary arterial hypertension (PAH) characterized by obliterative fibrosis of the small pulmonary veins and venules and/or capillary infiltration of the pulmonary interstitium leading to increased pulmonary vascular resistance and right ventricular dysfunction. [ Orphanet:431353 https://orcid.org/0000-0001-5208-3432 ]

Term info

database cross reference
  • Orphanet:431353 (MONDO:equivalentTo)
  • UMLS:CN237555 (MONDO:equivalentTo)
  • EFO:0009199 (MONDO:equivalentTo)
Subsets

disease_grouping, ordo_group_of_disorders

abbreviation
PVOD and/or PCH [ Orphanet:431353 ]

IAO 0000233

https://github.com/monarch-initiative/mondo/issues/5781

definition

A rare subgroup of pulmonary arterial hypertension (PAH) characterized by obliterative fibrosis of the small pulmonary veins and venules and/or capillary infiltration of the pulmonary interstitium leading to increased pulmonary vascular resistance and right ventricular dysfunction.

exactMatch

http://purl.obolibrary.org/obo/Orphanet_431353, http://linkedlifedata.com/resource/umls/id/CN237555

has exact synonym

PVOD and/or PCH

id

MONDO:0018554