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acquired purpura fulminans

^ http://purl.obolibrary.org/obo/MONDO_0018854

A life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children that is characterized by purpuric skin lesions and disseminated intravascular coagulation. PF may progress rapidly to multi-organ failure caused by thrombotic occlusion of small and medium-sized blood vessels. There are two forms of PF that are classified according to triggering mechanisms: acute infectious (the most common form), and idiopathic PF. [ Orphanet:49566 ]

Term info

database cross reference
  • UMLS:C4510896 (MONDO:equivalentTo)
  • Orphanet:49566 (MONDO:equivalentTo)
  • UMLS:C0043068 (Orphanet:49566/e)
  • MESH:D055665 (Orphanet:49566/e)
  • SCTID:725157006 (MONDO:equivalentTo)
  • MedDRA:10037556 (Orphanet:49566/e)
  • UMLS:CN205163 (MONDO:equivalentTo)
  • MESH:D014884 (Orphanet:49566/e)
Subsets

ordo_disease

closeMatch

http://identifiers.org/meddra/10037556

definition

A life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children that is characterized by purpuric skin lesions and disseminated intravascular coagulation. PF may progress rapidly to multi-organ failure caused by thrombotic occlusion of small and medium-sized blood vessels. There are two forms of PF that are classified according to triggering mechanisms: acute infectious (the most common form), and idiopathic PF.

exactMatch

http://purl.obolibrary.org/obo/Orphanet_49566, http://linkedlifedata.com/resource/umls/id/C4510896, http://identifiers.org/snomedct/725157006, http://linkedlifedata.com/resource/umls/id/CN205163

has exact synonym

acquired purpura fulminans, acquired PF

id

MONDO:0018854