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craniopharyngioma

^ http://purl.obolibrary.org/obo/MONDO_0018907

A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO) [ NCIT:C2964 ]

Term info

database cross reference
  • NCIT:C2964 (MONDO:equivalentTo)
  • MESH:D003397 (Orphanet:54595/e)
  • UMLS:C0010276 (Orphanet:54595/e)
  • MedDRA:10011318 (Orphanet:54595/e)
  • DOID:3840 (MONDO:equivalentTo)
  • EFO:1000209 (MONDO:equivalentTo)
  • ICD9:237.0 (MONDO:relatedTo)
  • ICDO:9350/1 (NCIT:C2964)
  • SCTID:189179009 (MONDO:equivalentTo)
  • Orphanet:54595 (MONDO:equivalentTo)
  • GARD:0010486 (MONDO:equivalentTo)
Subsets

ordo_disease

closeMatch

http://identifiers.org/meddra/10011318

definition

A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO)

exactMatch

http://identifiers.org/snomedct/189179009, http://purl.obolibrary.org/obo/NCIT_C2964, http://purl.obolibrary.org/obo/DOID_3840, http://identifiers.org/mesh/D003397, http://linkedlifedata.com/resource/umls/id/C0010276, http://purl.obolibrary.org/obo/Orphanet_54595

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0015514

has exact synonym

Rathke's pouch tumor, Rathke's pouch neoplasm, Rathke pouch neoplasm, craniopharyngioma (WHO grade I), craniopharyngioma (morphologic abnormality), tumor of Rathke's pouch, Rathke pouch tumor, neoplasm of Rathke's pouch, craniopharyngioma, benign

has related synonym

cystoma, craniopharyngeal duct tumor, Dysodontogenic epithelial tumor, Adamantinomatous tumor

id

MONDO:0018907