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enteropathy-associated T-cell lymphoma

^ http://purl.obolibrary.org/obo/MONDO_0019473

An uncommon mature T-cell lymphoma of intraepithelial lymphocytes. It usually arises from the small intestine, most commonly the jejunum or ileum. Other less frequent primary anatomic sites include the duodenum, stomach, colon, or outside the gastrointestinal tract. It is seen with increased frequency in regions with a high prevalence of celiac disease. [ NCIT:C4737 ]

Term info

database cross reference
  • UMLS:C0456889 (Orphanet:86880/e)
  • Orphanet:86880 (MONDO:equivalentTo)
  • ONCOTREE:EATL (MONDO:equivalentTo)
  • NCIT:C4737 (MONDO:exact-label-match)
  • SCTID:277654008 (MONDO:equivalentTo)
  • ICDO:9717/3 (NCIT:C4737)
  • MESH:D058527 (Orphanet:86880/e)
  • GARD:0009809 (MONDO:equivalentTo)
  • ICD9:202.70 (MONDO:relatedTo)
  • MedDRA:10022703 (Orphanet:86880/e)
Subsets

gard_rare, ordo_disease

abbreviation
ETTL [ Orphanet:86880 ]

abbreviation
EATCL [ GARD:0009809 ]

abbreviation
EATL [ ONCOTREE:EATL Orphanet:86880 ]

closeMatch

http://identifiers.org/meddra/10022703

comment

Editor note: consider moving ORDO class to SI subclass

definition

An uncommon mature T-cell lymphoma of intraepithelial lymphocytes. It usually arises from the small intestine, most commonly the jejunum or ileum. Other less frequent primary anatomic sites include the duodenum, stomach, colon, or outside the gastrointestinal tract. It is seen with increased frequency in regions with a high prevalence of celiac disease.

exactMatch

http://identifiers.org/snomedct/277654008, http://identifiers.org/mesh/D058527, http://purl.obolibrary.org/obo/Orphanet_86880, http://purl.obolibrary.org/obo/NCIT_C4737, http://linkedlifedata.com/resource/umls/id/C0456889

excluded subClassOf

http://purl.obolibrary.org/obo/MONDO_0018505

has exact synonym

enteropathy-associated T-cell lymphoma, type I, enteropathy associated T-cell lymphoma, EATL, ETTL, intestinal T-cell lymphoma, enteropathy-type T-cell lymphoma, EATL, type I

has related synonym

high-grade pleomorphic peripheral T-cell lymphoma, EATCL

id

MONDO:0019473

seeAlso

https://rarediseases.info.nih.gov/diseases/9809/enteropathy-associated-t-cell-lymphoma

Term relations