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pancreatic neuroendocrine tumor

^ http://purl.obolibrary.org/obo/MONDO_0019954


Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma). [ Orphanet:97253 ]

Term info

database cross reference
  • ONCOTREE:PANET (MONDO:equivalentTo)
  • Orphanet:97253 (MONDO:equivalentTo)
  • ICDO:8150/1 (NCIT:C27720)
  • NCIT:C27720 (MONDO:equivalentTo)
  • GARD:0013034 (MONDO:equivalentTo)
  • EFO:1000045 (MONDO:equivalentTo)
Subsets

disease_grouping, ordo_group_of_disorders

abbreviation
PANET [ ONCOTREE:PANET ]

definition

Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma).

exactMatch

http://purl.obolibrary.org/obo/NCIT_C27720, http://purl.obolibrary.org/obo/Orphanet_97253

has exact synonym

islet cell tumors - pancreas, well differentiated pancreatic endocrine neoplasm, well-differentiated NEN of pancreas, well-differentiated pancreatic NEN, pancreatic neuroendocrine tumor, islet cell tumor, islet cell tumors of the pancreas, well-differentiated pancreatic neuroendocrine neoplasm, well differentiated pancreatic endocrine tumor, pancreatic NET, well-differentiated neuroendocrine neoplasm of pancreas

has related synonym

neuroendocrine tumor of pancreas, PANET, pancreatic endocrine tumor

id

MONDO:0019954