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extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor

^ http://purl.obolibrary.org/obo/MONDO_0021039


A spectrum of malignant tumors arising from the soft tissues, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. Pain and the presence of a mass are the most common clinical symptoms. [ NCIT:C27293 ]

Term info

database cross reference
  • UMLS:C1333514 (NCIT:C27293)
  • DOID:4985 (MONDO:equivalentTo)
  • EFO:1000250 (MONDO:equivalentTo)
  • NCIT:C27293 (MONDO:equivalentTo)
definition

A spectrum of malignant tumors arising from the soft tissues, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. Pain and the presence of a mass are the most common clinical symptoms.

exactMatch

http://linkedlifedata.com/resource/umls/id/C1333514, http://purl.obolibrary.org/obo/DOID_4985, http://purl.obolibrary.org/obo/NCIT_C27293

has exact synonym

extraosseous Ewings sarcoma-primitive neuroepithelial tumor, extraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumor, extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor, extraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumor

has related synonym

extraosseous Ewing's tumor

id

MONDO:0021039