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abdominal cystic lymphangioma

^ http://purl.obolibrary.org/obo/MONDO_0021726


Abdominal cystic lymphangioma is a benign (noncancerous) malformation of the lymphatic vessels in the abdomen. These vessels carry lymph, a fluid that contains white blood cells that fight infection, throughout the body. The severity of the condition and the associated features vary from person to person. When present, signs and symptoms may include abdominal pain, an increase in waist circumference, an abdominal mass, intestinal obstruction, and/or volvulus (a twisting of the intestines). The cause of abdominal cystic lymphangioma is poorly understood; however, scientists suspect that it is a congenital anomaly. Most cases are diagnosed in people with no family history of the condition. Treatment varies based on the severity of the condition. People with small malformations that do not cause any symptoms may simply be followed with regular imaging studies to monitor for progression. Some of these cases may resolve spontaneously without treatment. When necessary, surgical excision is often the treatment of choice since it is associated with the lowest risk of recurrence.. [ GARD:0000439 ]

Term info

database cross reference
  • GARD:0000439 (MONDO:equivalentTo)
  • UMLS:C2930929 (MONDO:equivalentTo)
  • MESH:C535553 (MONDO:equivalentTo)
Subsets

gard_rare

abbreviation
RCL [ GARD:0000439 ]

definition

Abdominal cystic lymphangioma is a benign (noncancerous) malformation of the lymphatic vessels in the abdomen. These vessels carry lymph, a fluid that contains white blood cells that fight infection, throughout the body. The severity of the condition and the associated features vary from person to person. When present, signs and symptoms may include abdominal pain, an increase in waist circumference, an abdominal mass, intestinal obstruction, and/or volvulus (a twisting of the intestines). The cause of abdominal cystic lymphangioma is poorly understood; however, scientists suspect that it is a congenital anomaly. Most cases are diagnosed in people with no family history of the condition. Treatment varies based on the severity of the condition. People with small malformations that do not cause any symptoms may simply be followed with regular imaging studies to monitor for progression. Some of these cases may resolve spontaneously without treatment. When necessary, surgical excision is often the treatment of choice since it is associated with the lowest risk of recurrence..

exactMatch

http://linkedlifedata.com/resource/umls/id/C2930929, http://identifiers.org/mesh/C535553

has exact synonym

abdomen cystic lymphangioma

has related synonym

retroperitoneal cystic lymphangioma, RCL, abdominal retroperitoneal lymphangioma

id

MONDO:0021726

seeAlso

https://rarediseases.info.nih.gov/diseases/439/abdominal-cystic-lymphangioma

Term relations

Subclass of: